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长治这家医院攻克1例罕见病!

  • 2026-02-09 12:45:50
长治这家医院攻克1例罕见病!

近日,长治市中医研究所附属医院脑病科一病区成功救治一名罕见中枢神经系统血管炎引发反复脑梗死的患者。通过多学科协作(MDT)与先进影像学技术赋能,医疗团队精准锁定病因、优化治疗方案,帮助患者摆脱病情反复困境,目前患者症状已稳定,生命体征恢复正常。

据了解,58岁的男性患者因“双膝关节麻木”入院,初诊时疑似腰椎相关问题。然而次日,患者出现感觉异常症状,经磁共振(MRI)检查确诊为双侧额顶叶多发新鲜脑梗死。医疗团队随即启动抗血小板、强化降脂等常规治疗,患者症状初步好转,但仅3天后病情便再次发作,复查MRI显示新增多处新发脑梗死,症状较前更为明显,常规治疗方案陷入瓶颈。

患者第一次就诊,双侧大脑半球多发脑梗死

患者再次就诊,出现了新的脑梗死病灶

“患者双侧大脑半球的多发脑梗死分布在不同时间段、不同部位,这提示背后存在非常规病因。”脑病科一病区医疗团队迅速调整诊疗思路,首先通过血栓基因检测发现患者对他汀类药物反应特殊,及时优化降脂方案。为进一步明确病因,团队邀请医学影像科联合会诊,借助医院最新引进的3.0T磁共振成像仪开展“磁共振高分辨颅内血管壁成像”检查。

检查结果清晰显示,患者脑血管管壁存在多发环周增厚,右侧大脑前动脉闭塞且伴有管壁广泛强化,结合临床症状与影像特征,医学影像科团队初步判断患者罹患“中枢神经系统血管炎”。这一疾病属于少见且复杂的病症,病因尚未完全明确,其核心危害在于引发脑血管炎症,进而导致脑梗死反复发作,且因症状易与常见病症混淆,需依赖精准影像学检查才能确诊。

面对这一特殊病例,脑病科一病区立即组织多学科会诊。尽管患者血管炎抗体检查结果为阴性,但医疗团队综合影像特征与病情进展,经疑难病例讨论后果断启用激素冲击治疗——采用甲泼尼龙这一强效抗炎药物,抑制免疫反应、减轻血管壁炎症,阻断脑梗死进一步进展。

激素治疗前

激素治疗后

治疗一段时间后,患者症状得到显著改善。复查“磁共振高分辨颅内血管壁成像”显示,脑内多处血管壁强化程度显著减低,右侧大脑前动脉血管壁强化程度明显减少,标志着治疗取得关键性成效。目前患者症状稳定,血管壁炎症反应得到有效控制,患者及家属对治疗效果给予高度认可。

“此次病例的成功救治,关键在于精准诊断与个体化治疗的结合。”长治市中医研究所附属医院相关负责人表示,对于常规治疗无效的反复性脑梗死,需警惕血管炎等罕见潜在病因。此次诊疗过程既彰显了医院脑病科与医学影像科的专业诊疗水平,也体现了多学科协作体系的实战效能,更凸显了3.0T磁共振及“磁共振高分辨颅内血管壁成像”技术在捕捉血管壁细微病理改变、助力精准诊断中的核心作用。

未来,长治市中医研究所附属医院将持续深耕精准医疗,不断完善多学科协作机制,提升罕见病、疑难病诊疗能力,以更先进的技术、更优质的服务为广大患者的生命健康保驾护航。

原标题长治市中医研究所附属医院多学科协作,精准诊疗,成功诊治一例中枢神经系统血管炎
责编|王青平 编辑贾霄星  校对邢璐霞
出品黄河新闻网长治频道
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  1. CONNECT:[ UseTime:0.000407s ] mysql:host=127.0.0.1;port=3306;dbname=h460;charset=utf8mb4
  2. SHOW FULL COLUMNS FROM `fenlei` [ RunTime:0.000802s ]
  3. SELECT * FROM `fenlei` WHERE `fid` = 0 [ RunTime:0.000299s ]
  4. SELECT * FROM `fenlei` WHERE `fid` = 63 [ RunTime:0.000277s ]
  5. SHOW FULL COLUMNS FROM `set` [ RunTime:0.000518s ]
  6. SELECT * FROM `set` [ RunTime:0.000201s ]
  7. SHOW FULL COLUMNS FROM `article` [ RunTime:0.000508s ]
  8. SELECT * FROM `article` WHERE `id` = 465398 LIMIT 1 [ RunTime:0.002573s ]
  9. UPDATE `article` SET `lasttime` = 1771905676 WHERE `id` = 465398 [ RunTime:0.001303s ]
  10. SELECT * FROM `fenlei` WHERE `id` = 66 LIMIT 1 [ RunTime:0.000235s ]
  11. SELECT * FROM `article` WHERE `id` < 465398 ORDER BY `id` DESC LIMIT 1 [ RunTime:0.000391s ]
  12. SELECT * FROM `article` WHERE `id` > 465398 ORDER BY `id` ASC LIMIT 1 [ RunTime:0.003283s ]
  13. SELECT * FROM `article` WHERE `id` < 465398 ORDER BY `id` DESC LIMIT 10 [ RunTime:0.000679s ]
  14. SELECT * FROM `article` WHERE `id` < 465398 ORDER BY `id` DESC LIMIT 10,10 [ RunTime:0.003439s ]
  15. SELECT * FROM `article` WHERE `id` < 465398 ORDER BY `id` DESC LIMIT 20,10 [ RunTime:0.003186s ]
0.085844s